Scrotal hysterectomy in a male patient with mixed gonadal dysgenesis 46,XY(75%)/45,X(25%)

Publikation

Scrotal hysterectomy in a male patient with mixed gonadal dysgenesis 46,XY(75%)/45,X(25%)

Wissenschaftlicher Artikel/Review - 01.12.2007

Preusser Stefan, Diener Pierre-André, l'Allemand-Jander Dagmar, Schmid Sacha, Leippold Thomas, Brändle Michael, Schmid Hans-Peter

Zitation

Preusser S, Diener P, l'Allemand-Jander D, Schmid S, Leippold T, Brändle M, Schmid H. Scrotal hysterectomy in a male patient with mixed gonadal dysgenesis 46,XY(75%)/45,X(25%). Urology 2007; 70:1223.e7-9.

Art

Wissenschaftlicher Artikel/Review (Englisch)

Zeitschrift

Urology 2007; 70

Veröffentlichungsdatum

01.12.2007

eISSN (Online)

1527-9995

Seiten

1223.e7-9

Kurzbeschreibung/Zielsetzung

We report on a 20-year-old man in whom endocrinological investigation owing to dysmorphic signs characteristic for Turner syndrome revealed mixed gonadal dysgenesis. The patient was referred to us for further diagnostic investigations on a right intrascrotal tumour. Both testes were intrascrotal and hypotrophic with normal testosterone production. Surgical investigation showed a circumscribed tumor that proved to be a rudimentary uterus without evidence of malignancy at histological examination. Biopsies from both tested showed no signs of malignant disease. After removal of the tumor, we decided not to remove the testes prophylactically because of the male phenotype and the sufficient testosterone production.