Ebstein's Anomaly of the Tricuspid Valve: an Overview of Pathology and Management

Publication

Ebstein's Anomaly of the Tricuspid Valve: an Overview of Pathology and Management

Journal Paper/Review - Oct 9, 2020

Possner Mathias, Gensini Francisco J, Mauchley David C, Krieger Eric V, Steinberg Zachary L

Citation

Possner M, Gensini F, Mauchley D, Krieger E, Steinberg Z. Ebstein's Anomaly of the Tricuspid Valve: an Overview of Pathology and Management. Curr Cardiol Rep 2020; 22:157.

Type

Journal Paper/Review (English)

Journal

Curr Cardiol Rep 2020; 22

Publication Date

Oct 9, 2020

Issn Electronic

1534-3170

Pages

157

Brief description/objective

PURPOSE OF REVIEW
Ebstein's anomaly (EA) is a rare, but complex form of congenital heart disease consisting of a right ventricular myopathy and morphologic tricuspid valve disease leading to a high incidence of right ventricular dysfunction and arrhythmias. This review offers an updated overview of the current understanding and management of patients with EA with a focus on the adult population.

RECENT FINDINGS
Increased understanding of anatomic accessory atrioventricular pathways in EA has resulted in an improvement in ablation techniques and long-term freedom of atrial arrhythmia recurrence. Despite an improvement in understanding and recognition of EA, significant disease heterogeneity and complex treatment options continue to challenge providers, with the best outcomes achieved at expert congenital heart disease centers.