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Ebstein's Anomaly of the Tricuspid Valve: an Overview of Pathology and Management

Mathias Possner, Francisco J Gensini, David C Mauchley, Eric V Krieger & Zachary L Steinberg

abstract

PURPOSE OF REVIEW
Ebstein's anomaly (EA) is a rare, but complex form of congenital heart disease consisting of a right ventricular myopathy and morphologic tricuspid valve disease leading to a high incidence of right ventricular dysfunction and arrhythmias. This review offers an updated overview of the current understanding and management of patients with EA with a focus on the adult population.

RECENT FINDINGS
Increased understanding of anatomic accessory atrioventricular pathways in EA has resulted in an improvement in ablation techniques and long-term freedom of atrial arrhythmia recurrence. Despite an improvement in understanding and recognition of EA, significant disease heterogeneity and complex treatment options continue to challenge providers, with the best outcomes achieved at expert congenital heart disease centers.
   
citation Possner M, Gensini F J, Mauchley D C, Krieger E V, Steinberg Z L. Ebstein's Anomaly of the Tricuspid Valve: an Overview of Pathology and Management. Curr Cardiol Rep 2020; 22:157.
   
type journal paper/review (English)
date of publishing 09-10-2020
journal title Curr Cardiol Rep (22/12)
ISSN electronic 1534-3170
pages 157
PubMed 33037480
DOI 10.1007/s11886-020-01412-z